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Vol. 10. Issue 2.
Pages 165-171 (March - April 2004)
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Vol. 10. Issue 2.
Pages 165-171 (March - April 2004)
CASO CLÍNICO/CLINICAL CASE
Open Access
Derrame pleural recidivante com macroglobulinemia – caso clínico com revisão da literatura
Recurrent pleural effusion with macroglobulinemia – case report with revision of the literature
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João Moura e Sá*
* Assistente Graduado de Pneumologia – Departamento de Pneumologia. Centro Hospitalar de Vila Nova de Gaia
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RESUMO

Descrevemos um caso de derrame pleural recidivante crónico num homem de 73 anos com infiltração pleural linfoplasmocitária e gamopatia monoclonal (IgM k), sem outras manifestações da doença de Waldenström (DW). O doente foi tratado sintomaticamente, mantendo bom estado geral durante um período de três anos. Faleceu de causa não relacionada com a patologia referida, acidente vascular cerebral. Procedemos à revisão da literatura procurando definir as diferentes apresentações da DW.

REV PORT PNEUMOL 2004; X (2): 165-171

Palavras-chave:
derrame pleural
gamopatia monoclonal
macroglobulinemia de Waldenström´s
ABSTRACT

We describe a case of chronic relapsing pleural effusion in a 73 year old male with lymphopalsmocytic pleural infiltration and monoclonal gamopathy (IgMk), and no other manifestation of Waldenström´s Disease (W.D.). The patient was treated symptomatically and remained in good general condition up to his death from unrelated causes after 3 years of evolution. We reviewed the literature trying to define the different presentations of W.D.

REV PORT PNEUMOL 2004; X (2): 165-171

Key Words:
pleural effusion
monoclonal gamopathy
Waldenström´s macroglobulinemia
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Copyright © 2004. Sociedade Portuguesa de Pneumologia/SPP
Pulmonology
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