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RESUMO
A Fibrose Quística no momento actual não constitui uma doença exclusiva da idade pediátrica; o n.° de doentes adultos aumenta anualmente, preveudo-se que em 1996 metade dos doentes atingirão a idade adulta. A propósito da abert ura de uma Consulta para Adultos com Fibrose Quística, avalia-se a sua actividade ao fim do 1.° ano, e tecem-se algumas eonsiderações sobre o diagnóstico de Fibrose Quistíca na idade adulta.
Palavras-chave:
Fibrose Quística
adulto
criança
SUMMARY
Cystic Fibrosis is present no longer a disease of childhood; the number of adult patients has been increasing year by year, and by 1996 half of diagnosed patients are expected to reach adulthood.
The activity of a resently started clinic for adult cystic fibrosis patients is analysed at the end of its first year and the diagnosis of cystic fibrosis in adulthood is discussed.
Key-words:
Cystic Fibrosis
Adult
Children
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