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Vol. 8. Issue 1.
Pages 87-95 (January - February 2002)
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Vol. 8. Issue 1.
Pages 87-95 (January - February 2002)
CASO CLÍNICO/CLINICAL CASE
Open Access
Granulomatose de Wegener – Forma limitada
Limited Wegener‘s Granulomatosis
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4894
I. Gil1, J. Porto2, B. Fernandes3, M. Gonçalo4, L. Carvalho5, J.D. Vieira6, J.J. Moura7
1 Interna do Internato Complementar de Pneumologia dos Hospitais da Universidade de Coimbra
2 Interno do Internato Complementar de Medicina Interna dos Hospitais da Universidade de Coimbra
3 Interna do Internato Complementar de Dermatologia dos Hospitais da Universidade de Coimbra
4 Assistente Hospitalar Graduada de Dermatologia dos Hospitais da Universidade de Coimbra
5 Professora Auxiliar de Anatomia Patológica da Faculdade de Medicina e dos Hospitais da Universidade de Coimbra
6 Assistente Hospitalar Graduado de Medicina Interna dos Hospitais da Universidade de Coimbra
7 Professor da Faculdade de Medicina e Director do Serviço de Medicina II dos Hospitais da
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RESUMO

Doente do sexo feminino, 53 anos de idade, internada por lesões nodulares pulmonares sugestivas de doença metastática.

Antecedentes de Doença de Graves e de Pyoderma gangrenosum.

Biópsia pulmonar compatível com Granulomatose de Wegener.

REV PORT PNEUMOL 2002; VIII (1): 87-93

Palavras-chave:
granulomatose
Wegener
forma limitada
vasculite
ABSTRACT

Female, 53 years old, with nodular lung lesions suggesting metastatic disease.

This patient had clinical antecedents of Graves disease and Pyoderma gangrenosum.

The lung biopsy was compatible with Wegener’ Granulomatosis.

REV PORT PNEUMOL 2002; VIII (1): 87-93

Key-words:
granulomatosis
Wegener
limited
vasculitis
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BIBLIOGRAFIA
[1.]
Armin Schnabel, Csernok Elena, Braun Jorg, Wolfgang L. Gross.
Activation of neutophils, eosinophils, and limphocytes in the lower respiratory tract in Wegener`s Granulomatosis.
Am J Respir Crit Care Med, 161 (2000), pp. 399-405
[2.]
Carol A. Langford, Gary S. Hoffman.
Wegener’s granulomatosis.
Thorax, 54 (1999), pp. 629-637
[3.]
Savage Cos, L. Harper, D. Adu.
Primary systemic vasculitis.
Lancet, 394 (1997), pp. 553-558
[4.]
A.S. Fauci, B.F. Haynes, P. Katz.
Wegener’s granulomatosis: prospective clinical and therapeutic experience with 85 patients for 21 years.
Ann Intern Med, 98 (1983), pp. 76-85
[5.]
G.S. Hoffman, G.S. Kerr, R.Y. Leavitt.
Wegener granulomatosis: an analysis of 158 patients.
Ann Intern Med, 116 (1992), pp. 488-494
[6.]
D.J. Davies, J.E. Moran, J.F. Niall.
Segmental necrotising glomerulonephritis with antineutrophil antibody: possible arbovirus aetiology?.
BMJ, 285 (1982), pp. 606
[7.]
D.E.R. Van, F.J. Woude, S. Lobatto, H. Permin.
Autoantibodies aginst neutrophils and monocytes: tool for diagnosis and marker of disease activitiy in Wegener’s granulomatosis.
Lancet, (1985), pp. 425-429
[8.]
C.A. Langford.
The diagnostic utility of c-ANCA in Wegener’s granulomatosis.
Clev Clin J Med, 65 (1988), pp. 135-140
[9.]
Vignon-Pennamen Dominique, Zelinsky-Gurung Ariane, Janssen Fabienne, Frija Jacques, Wallach Daniel.
Pyoderma Gangrenosum With Pulmonar Involvement.
Arch Dermatol, 125 (1989), pp. 1239-1242
[10.]
M.S. Daound, L.E. Gibson, R.A. Deremee, U. Specks, R.A. El-Azhary, W.P. Su.
Cutaneous Wegener’s granulomatosis: clinical, histopathologic and immunopathologic features of thirty patients.
J Am Acad Dermatol, 31 (1994), pp. 605-612
[11.]
Koert M. Dolman, Rijk O.B. Gans, T.H.J. Vervaat, G. Zevenbergen, Maingay Dick, Goldschmeding Roel.
Vasculitis and antineutrophil cytoplasmatic autoantibodies associated with propylthiouracil therapy.
The Lancet, 342 (1993), pp. 651-652
[12.]
Michael Pillinger, Roland Staud.
Wegener’s granulomatosis in a patient receiving propylthiouracil for graves´disease.
Seminars in Arthritis and Rheumatism, 28 (1998), pp. 124-129
[13.]
N.O.H. Jaeduk Yoshimura, Asarl Tomoki, Hamada Noboru, Makino Fuminori, L.T.O. Kuniniko.
Clinical Endocrinology, 54 (2001), pp. 651-654
[14.]
Hyon K. Choi, Peter A. Merkel, Alexander M. Walker, John L. Niles.
Arthritis and Rheumatism, 43 (2000), pp. 405-413
Copyright © 2002. Sociedade Portuguesa de Pneumologia/SPP
Pulmonology
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