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Vol. 15. Issue 3.
Pages 543-552 (May - June 2009)
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Vol. 15. Issue 3.
Pages 543-552 (May - June 2009)
Caso Clínico/Case Report
Open Access
Sarcoidose: Uma forma rara de apresentação
Sarcoidosis: A less common presentation
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Jessica Cemlyn-Jones1,
Corresponding author
jcemlynjones@yahoo.com

Departamento de Ciências Pneumológicas e Alergológicas dos Hospitais da Universidade de Coimbra, Director de Serviço: Dr. Mário Chaves Loureiro, Director de Departamento: Prof. Doutor Manuel Fontes Baganha, Av. Bissaya Barreto e Praceta Prof. Mota Pinto, 3000-075 Coimbra.
, Fernanda Gamboa2, Luísa Teixeira3, João Bernardo4, Carlos Robalo Cordeiro5
1 Interna Complementar de Pneumologia, Hospitais da Universidade de Coimbra
2 Assistente Hospitalar de Pneumologia, Hospitais da Universidade de Coimbra
3 Chefe de Serviço de Radiodiagnóstico, Hospitais da Universidade de Coimbra
4 Chefe de Serviço de Cirurgia Cardiotorácica, Hospitais da Universidade de Coimbra
5 Coordenador da Unidade Funcional de Técnicas de Diagnóstico e Terapêutica, Hospitais da Universidade de Coimbra
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Resumo

A apresentação clínica da sarcoidose é diversa e em mais de 90% dos casos existe envolvimento pulmonar. Os achados radiológicos mais frequentes aquan-do do diagnóstico são a presença de adenopatias hila-res e infiltrados pulmonares.

Os autores apresentam o caso de uma doente jovem cuja radiografia torácica apresentava múltiplos nódulos bilaterais. A biópsia cirúrgica revelou a presença de granulomas não necrotizantes com células gigantes multinucleadas, compatível com sarcoidose. Apesar de se tratar de uma sarcoidose pulmonar estádio III, a doente apresentava-se assintomática, o estudo funcional ventilatório era normal e não havia si-nais de envolvimento extratorácico, pelo que foi decidido não iniciar tratamento. Houve remissão espontânea das lesões, comprovada em tomografia computorizada de alta resolução após um ano.

Rev Port Pneumol 2009; XV (3): 543-552

Palavras-chave:
Sarcoidose
múltiplos nódulos pulmonares bilaterais
remissão espontânea
Abstract

The clinical presentation of sarcoidosis is diverse and in over 90% of patients there is pulmonary involvement. The most common features of the radiographic findings at the time of diagnosis are bilateral hilar lymphadenopathy and pulmonary infiltration.

The authors report the case of a young female patient who presented with multiple bilateral nodular shadows on chest radiograph. Surgical biopsy revealed non-necrotizing granulomas with occasional multi-nucleated giant cells compatible with sarcoidosis. Al-though this was a case of stage III pulmonary disease, the patient was asymptomatic, lung function tests were normal and there were no signs of extrathoracic involvement. Spontaneous remission occurred with-out treatment as shown on high resolution CT scan follow-up, one year later.

Rev Port Pneumol 2009; XV (3): 543-552

Key-words:
Sarcoidosis
multiple bilateral nodular shadows
spontaneous remission
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Bibliografia/Bibliography
[1.]
Z.C. Traill, G.F. Maskell, F.V. Gleesson.
High-resolution CT findings of pulmonary sarcoidosis.
AJR Am J Roent-genol, 168 (1997), pp. 1557-1560
[2.]
H. Nakamura, K. Kashiwabara, T. Watanabe, H. Yagyu, T. Kiguchi, K. Matsuoka.
Sarcoidosis with multiple nodular shadows in bilateral lung fields.
Intern Med, 34 (1995), pp. 1144-1145
[3.]
V.M. Hamper, E.K. Fishman, N.F. Khouri, C.T. Jonhs, K.P. Wong, S.S. Siegelman.
Typical and atypical CT manifestations of pulmonary sarcoidosis.
J Comput Assist Tomogr, 10 (1986), pp. 928-936
[4.]
G. Hillerdal, E. Nou, K. Osterman, B. Schmekel.
Sarcoidosis: epidemiology and prognosis. A 15-year European study.
Am Rev Respir Dis, 130 (1984), pp. 29-32
[5.]
J.C. Johns, T.M. Michele.
The clinical management of sarcoidosis. A 50-year experience at the Johns Hopkins Hospital.
Medicine, 78 (1999), pp. 65-111
[6.]
ATS/ERS/WASOG statement on sarcoidosis. Sar-coidosis Statement Committee. American Thoracic Society. European Respiratory Society.
World Association for Sarcoidosis and Other Granulomatous Disorders.
Eur Respir J, 14 (1999), pp. 735-737
[7.]
U. Costabel.
Sarcoidosis: Clinical update.
Eur Respir J Suppl, 32 (2001), pp. 56s-68s
[8.]
L. Newman, C. Rosen, L. Maier.
Medical progress: Sarcoidosis.
N Engl J Med, 336 (1997), pp. 1224-1234
[9.]
A. Luis Segorbe.
Sarcoidose.
Tratado de Pneumologia da Sociedade Portuguesa de Pneumologia, pp. 1327-1338
[10.]
M. Remy-Jardin, F. Giroud, J. Remy, L. Wattine, B. Wallaert, A. Duhamel.
Pulmonary sarcoidosis: role of CT in the evaluation of disease activity and functional impairment in prognosis assessment.
Radiology, 191 (1994), pp. 675-680
[11.]
J.C. Grutters, J.M. van der Bosch.
Corticosteroid treatment in sarcoidosis.
Eur Respir J, 28 (2006), pp. 627-648
[12.]
R.P. Baughman, U. Costabel, R.M. du Bois.
Treatment of sarcoidosis.
Clin Chest Med, 29 (2008), pp. 533-548
[13.]
R.P. Baughman, E.E. Lower.
Therapy for sarcoidosis.
Eur Respir Mon, 32 (2005), pp. 301-315
[14.]
S. Newman, Wasfi Y. Sarcoidosis.
Diffuse Parenchymal Lung Disease, pp. 128-138
Copyright © 2009. Sociedade Portuguesa de Pneumologia/SPP
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