Síndroma de Churg-Strauss – a propósito de um caso clínico

Oliveira, Susana; Mendonça, Catarina; Ambar, José Eduardo; Mendes, Berta

doi:10.1016/S0873-2159(15)30486-4

Article information

Resumo

A síndroma de Churg-Strauss (SCS) é uma vasculite sistémica pouco comum, que atinge preferencialmente vasos de pequeno calibre, envolve múltiplos órgãos e surge quase sempre associada a asma e eosinofilia.

Os autores fazem uma revisão sobre esta doença e discutem o seu diagnóstico diferencial a propósito do caso clínico de uma mulher com diagnóstico de asma brônquica que aos 65 anos inicia quadro compatível com SCS.

Rev Port Pneumol 2005; XI (1): 73-83

Palavras-Chave:

Churg-Strauss

asma

vasculite

ANCA

Abstract

Churg-Strauss syndrome (CSS) is a rare systemic vasculitis, that essentially affects medium-sized vessels, involves multiple organs and in the majority of cases is related to asthma and eosinophilia.

The authors make a review of this disease and discuss its differential diagnosis presenting the case of a woman with asthma that at the age of 65 is diagnosed with CSS.

Rev Port Pneumol 2005; XI (1): 73-83

Key words:

Churg-Strauss

asthma

vasculitis

ANCA

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