Caso Clínico/Case Report
Hemotórax espontâneo em doente com neurofibromatose tipo I – A propósito de um caso clínico
Spontaneous hemothorax in a neurofibromatosis type I patient – A case report
Alexandra Bento1,
, Ana Paula Gonçalves2
Corresponding author
alexitbento@gmail.com
Unidade de Saúde Local EPE, Guarda, Serviço de Pneumologia Avenida Rainha D. Amélia, 6300 Guarda.
Unidade de Saúde Local EPE, Guarda, Serviço de Pneumologia Avenida Rainha D. Amélia, 6300 Guarda.
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Amélia, 6300 Guarda." ] ] ] ] "titulosAlternativos" => array:1 [ "en" => array:1 [ "titulo" => "Spontaneous hemothorax in a neurofibromatosis type I patient – A case report" ] ] "pdfFichero" => "main.pdf" "tienePdf" => true "fechaRecibido" => "2009-03-03" "fechaAceptado" => "2009-04-01" "PalabrasClave" => array:2 [ "pt" => array:1 [ 0 => array:4 [ "clase" => "keyword" "titulo" => "Palavras-chave" "identificador" => "xpalclavsec570202" "palabras" => array:2 [ 0 => "Neurofibromatose" 1 => "hemotórax espontâneo" ] ] ] "en" => array:1 [ 0 => array:4 [ "clase" => "keyword" "titulo" => "Key-words" "identificador" => "xpalclavsec570203" "palabras" => array:2 [ 0 => "Neurofibromatosis" 1 => "spontaneous hemothorax" ] ] ] ] "tieneResumen" => true "resumen" => array:2 [ "pt" => array:2 [ "titulo" => "Resumo" "resumen" => "<span id="as0005" class="elsevierStyleSection elsevierViewall"><p id="sp0005" class="elsevierStyleSimplePara elsevierViewall">O hemotórax espontâneo é uma complicação rara e potencialmente fatal da neurofibromatose. Vários mecanismos patológicos são descritos para a vasculopatia associada à doença: a) invasão dos vasos por tumores adjacentes, como shwannoma, neurofibroma ou neu-rofibrosarcoma; b) displasia vascular com formação de aneurismas e estenoses<span class="elsevierStyleSup">6,7,9</span>. Outros mecanismos envolvidos podem incluir patologias pleuropulmonares (in-fecções com necrose, embolia pulmonar, endometriose, neoplasias) e discrasia sanguínea. Os autores relatam o caso de uma jovem de 33 anos, que recorreu ao serviço de urgência por toracalgia superior direita, contínua, irradiando para o ombro e escápula homolaterais, sem factores de agravamento nem de alívio e com oito dias de evolução.</p><p id="sp0010" class="elsevierStyleSimplePara elsevierViewall"><span class="elsevierStyleBold">Rev Port Pneumol 2009; XV (5): 937-941</span></p></span>" ] "en" => array:2 [ "titulo" => "Abstract" "resumen" => "<span id="as0010" class="elsevierStyleSection elsevierViewall"><p id="sp0015" class="elsevierStyleSimplePara elsevierViewall">Spontaneous hemothorax is a rare and potentially lethal neurofibromatosis’ complication. Several patho-logical mechanisms may explain the associated vasculopathy: a) direct vascular invasion from adjacent tumors such as Shwannoma, neurofibroma or neuro-fibrosarcoma; b) vascular dysplasia with stenotic or aneurysm formation<span class="elsevierStyleSup">6,7,9</span>. Other mechanisms involved may include pleuropulmonar pathologies (necrotizing infections, pulmonary embolism, endometriosis, neoplasms) and blood dyscrasias. The authors describe a case of a 33 years old female, who went to the ER Service complaining with right persistent hemithoracic pain, extending to the ipsilateral shoulder and shoulder blade, without aggravation or relieving factors, since the last 8 days.</p><p id="sp0020" class="elsevierStyleSimplePara elsevierViewall"><span class="elsevierStyleBold">Rev Port Pneumol 2009; XV (5): 937-941</span></p></span>" ] ] "lecturaRecomendada" => array:1 [ 0 => array:3 [ "vista" => "all" "titulo" => "<span class="elsevierStyleSectionTitle" id="st0025">Bibliografia</span>" "seccion" => array:1 [ 0 => array:2 [ "vista" => "all" "bibliografiaReferencia" => array:9 [ 0 => array:3 [ "identificador" => "bb0005" "etiqueta" => "1." 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"referencia" => array:1 [ 0 => array:2 [ "contribucion" => array:1 [ 0 => array:2 [ "titulo" => "Tratado de pneumologia. Sociedade Portuguesa de Pneumologia" "autores" => array:1 [ 0 => array:2 [ "etal" => true "autores" => array:2 [ 0 => "M.J.M. Gomes" 1 => "R. Sotto-Mayor" ] ] ] ] ] "host" => array:1 [ 0 => array:1 [ "LibroEditado" => array:4 [ "titulo" => "Hemotórax, capítulo" "paginaInicial" => "1505" "serieVolumen" => "115" "serieFecha" => "2003" ] ] ] ] ] ] 3 => array:3 [ "identificador" => "bb0020" "etiqueta" => "4." "referencia" => array:1 [ 0 => array:2 [ "contribucion" => array:1 [ 0 => array:2 [ "titulo" => "Hemothorax in type I neurofibromatosis" "autores" => array:1 [ 0 => array:2 [ "etal" => true "autores" => array:1 [ 0 => "Geiorge P. Teitlbaum" ] ] ] ] ] "host" => array:1 [ 0 => array:1 [ "Revista" => array:6 [ "tituloSerie" => "Ann Thorac Surg" "fecha" => "1998" "volumen" => "66" "paginaInicial" => "569" "paginaFinal" => "571" "link" => array:1 [ 0 => array:2 [ "url" => "https://www.ncbi.nlm.nih.gov/pubmed/9725414" "web" => "Medline" ] ] ] ] ] ] ] ] 4 => array:3 [ "identificador" => "bb0025" "etiqueta" => "5." "referencia" => array:1 [ 0 => array:2 [ "contribucion" => array:1 [ 0 => array:1 [ "autores" => array:1 [ 0 => array:2 [ "etal" => true "autores" => array:3 [ 0 => "B.F. Thomas" 1 => "A.J. Richard" 2 => "W. Klaus" ] ] ] ] ] "host" => array:1 [ 0 => array:1 [ "LibroEditado" => array:7 [ "titulo" => "Atlas e texto de dermatologia" "paginaInicial" => "440" "paginaFinal" => "443" "edicion" => "4" "serieVolumen" => "13" "serieTitulo" => "Neurofibromatose, secção" "serieFecha" => "2001" ] ] ] ] ] ] 5 => array:3 [ "identificador" => "bb0030" "etiqueta" => "6." "referencia" => array:1 [ 0 => array:2 [ "contribucion" => array:1 [ 0 => array:2 [ "titulo" => "Spontaneous haemothorax associated with Von Recklinghausen’s disease: review of occurrence in Japan" "autores" => array:1 [ 0 => array:2 [ "etal" => true "autores" => array:3 [ 0 => "M. Hiroyuki" 1 => "T. Osamu" 2 => "K. Harubumi" ] ] ] ] ] "host" => array:1 [ 0 => array:1 [ "Revista" => array:6 [ "tituloSerie" => "Thorax" "fecha" => "1997" "volumen" => "52" "paginaInicial" => "577" "paginaFinal" => "578" "link" => array:1 [ 0 => array:2 [ "url" => "https://www.ncbi.nlm.nih.gov/pubmed/9227730" "web" => "Medline" ] ] ] ] ] ] ] ] 6 => array:3 [ "identificador" => "bb0035" "etiqueta" => "7." "referencia" => array:1 [ 0 => array:2 [ "contribucion" => array:1 [ 0 => array:2 [ "titulo" => "Massive spontaneous hemothorax associated with Von Recklinghausen’s disease" "autores" => array:1 [ 0 => array:2 [ "etal" => true "autores" => array:2 [ 0 => "V. Mohammad" 1 => "M. Meetra" ] ] ] ] ] "host" => array:1 [ 0 => array:2 [ "doi" => "10.1016/j.athoracsur.2006.02.010" "Revista" => array:6 [ "tituloSerie" => "Ann Thorac Surg" "fecha" => "2006" "volumen" => "82" "paginaInicial" => "1500" "paginaFinal" => "1501" "link" => array:1 [ 0 => array:2 [ "url" => "https://www.ncbi.nlm.nih.gov/pubmed/16996963" "web" => "Medline" ] ] ] ] ] ] ] ] 7 => array:3 [ "identificador" => "bb0040" "etiqueta" => "8." "referencia" => array:1 [ 0 => array:1 [ "referenciaCompleta" => "<a href="http://www.radiologiaclinicacadecampinas.com.br/info_24.htm">http://www.radiologiaclinicacadecampinas.com.br/info_24.htm</a>." ] ] ] 8 => array:3 [ "identificador" => "bb0045" "etiqueta" => "9." 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Article information
ISSN: 08732159Original language: Portuguese
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