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Vol. 14. Issue 4.
Pages 541-544 (July - August 2008)
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Vol. 14. Issue 4.
Pages 541-544 (July - August 2008)
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Primary tracheobronchial amyloidosis – Two case reports
Amiloidose traqueobrônquica primária – A propósito de dois casos clínicos
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Sandra Saleiro1,4, Venceslau Pinto Hespanhol2,4, Adriana Magalhães3,4
1 Interna Complementar de Pneumologia
2 Chefe de Serviço de Pneumologia; Director do Serviço de Pneumologia do Hospital de São João; Professor Agregado da Faculdade de Medicina da Universidade do Porto
3 Assistente Hospitalar Graduada de Pneumologia
4 Hospital de São João, Alameda Prof. Hernâni Monteiro 4202-451 – Porto – Portugal
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Abstract

Primary tracheobronchial amyloidosis is a form of respiratory amyloidosis, characterised by insoluble amyloid fibril proteins deposits along the airways wall. It is an uncommon disease, requiring a tissue sample to establish the definite diagnosis based on specific pathological features.

The authors report two cases of tracheobronchial amyloidosis, describing their symptoms and the diagnostic and therapeutic procedures that were performed.

Key-words:
Amyloidosis
tracheobronchial
Resumo

A amiloidose traqueobrônquica primária é uma forma de amiloidose respiratória, caracterizada pela presença de depósitos insolúveis de proteína fibrilar amilóide, ao longo da parede das vias aéreas. É uma doença pouco frequente, sendo necessário uma amostra de tecido para estabelecer o diagnóstico definitivo, com base em características histológicas específicas. Os autores relatam dois casos clínicos de amiloidose traqueobrônquica, descrevendo os seus sintomas e os procedimentos diagnósticos e terapêuticos que foram efectuados.

Palavras-chave:
Amiloidose
traqueobrônquica
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Copyright © 2008. Sociedade Portuguesa de Pneumologia
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