Article information
Resumo
A síndroma de Churg-Strauss (SCS) é uma vasculite sistémica pouco comum, que atinge preferencialmente vasos de pequeno calibre, envolve múltiplos órgãos e surge quase sempre associada a asma e eosinofilia.
Os autores fazem uma revisão sobre esta doença e discutem o seu diagnóstico diferencial a propósito do caso clínico de uma mulher com diagnóstico de asma brônquica que aos 65 anos inicia quadro compatível com SCS.
Rev Port Pneumol 2005; XI (1): 73-83
Palavras-Chave:
Churg-Strauss
asma
vasculite
ANCA
Abstract
Churg-Strauss syndrome (CSS) is a rare systemic vasculitis, that essentially affects medium-sized vessels, involves multiple organs and in the majority of cases is related to asthma and eosinophilia.
The authors make a review of this disease and discuss its differential diagnosis presenting the case of a woman with asthma that at the age of 65 is diagnosed with CSS.
Rev Port Pneumol 2005; XI (1): 73-83
Key words:
Churg-Strauss
asthma
vasculitis
ANCA
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Bibliografia
[1.]
A. Abril.
The Churg-Strauss Syndrome: review and update.
Seminars in Arthritis and Rheumatism, 2 (2003), pp. 106-114
[2.]
A.T. Masi, G.G. Hunder, J.T. Lie.
The American College of Rheumatology 1990 criteria for the classification of Churg-Strauss syndrome (allergic granulomatosis and angiitis).
Arthritis Rheum, 33 (1990), pp. 1094-1100
[3.]
J.C. Jennette, R.J. Falk, K. Andrassy.
Nomeclature of systemic vasculitidis. Proposal of an international consensus conference.
Arthritis Rheum, 2 (1994), pp. 187-192
[4.]
B. Hellminch, S. Ehlers, E. Csernok.
Update on the pathogenesis of Churg-Strauss syndrome.
Clin Exp Rheumatol, 21 (2003), pp. S69-S77
[5.]
L.P. Guillevin, H. Visser, L.H. Noel, et al.
Antineutrophil cytoplasm antibodies (ANCA) in systemic polyarteritis nodosa with hepatitis B virus infection and Churg-Strauss syndrome. 62 patients.
J Rheumatol, 20 (1993), pp. 1345-1349
[6.]
M. Muschen, U. Warskulat, A. Perniok, et al.
Involvement of soluble CD 95 in Churg-Strauss syndrome.
Am J Pathol, 155 (1999), pp. 915-925
[7.]
J.G. Lanham, K.B. Elkon, C.D. Pusey, et al.
A clinical approach to the Churg-Stauss syndrome”.
Medicine, 83 (1994), pp. 65-81
[9.]
K.R. Chen, Y. Ohata, M. Sakurai, H. Nakayama.
Churg-Strauss syndrome: report of a case without pre-existing asthma.
J Dermatol, 19 (1992), pp. 40-47
[10.]
L. Guillevin, P. Cohen, M. Gayraud, et al.
Churg-Strauss syndrome. Clinical study and long term follow-up of 96 patients.
Medicine (Baltimore), 78 (1999), pp. 26
[11.]
Imre Noth, Mary E. Strek, Alan R. Leff.
Churg- Strauss syndrome.
Lancet, 361 (2003), pp. 587-594
[12.]
N. Hattori, M. Ichimura, M. Nagamatsu, et al.
Clinicopathological features of Churg-Stauss syndromeassociated neuropathy.
Brain, 122 (1999), pp. 427-439
[13.]
J.G. Lanham, K.B. Elkon, C.D. Pusey, et al.
Systemic vasculitis with asthma and eosinophilia: a clinical approach to the Churg-Strauss syndrome.
Medicine (Baltimore), 63 (1984), pp. 65-81
[14.]
P.B. Hasley, W.P. Follansbee, J.L. Coulehan.
Cardiac manifestations of Churg-Strauss syndrome: Report of a case and review of the literature.
Am Heart J, 120 (1990), pp. 996
[15.]
J. Churg, L. Strauss.
Allergic angiitis, and periarteritis nodosa.
Am J Pathol, 27 (1951), pp. 277
[16.]
C. Hass, C. Geneau, J.M. Odinot, et al.
L’angeite allergique avec granulomatosis: syndrome de Churg-Strauss. Étude retrospective de 16 observations.
Ann Med Interne, 142 (1991), pp. 335-342
[17.]
D.I. Conn, F.C. MaDuffie, K.E. Holley, et al.
Immunologic mechanisms in systemic vasculitis.
Mayo Clin Proc, 51 (1976), pp. 511-518
[18.]
Y.H. Choi, J.G. Im, B.K. Han, et al.
Thoracic manifestations of Churg-Strauss syndrome: Radiologic and clinical findings.
Chest, 117 (2000), pp. 117
[19.]
D.C. Todd, D.W. Cockcroft.
Prolonged survival in Churg-Strauss syndrome.
Ann Allergy Asthma Immunol, 92 (2004), pp. 92-93
[21.]
J.T. Lie.
Nomeclature and classification of vasculitis. Plus ça change, plus c’est la meme chose (editorial).
Arthritis Rheum, 37 (1994), pp. 181-186
[22.]
J.C. Jennette, R.J. Falk.
Small-vessel vasculitis.
N Engl J Med, 337 (1997), pp. 1512
[23.]
W. Kelley, E. Harris, S. Ruddy, C. Sledge.
5ª edition, pp. 1079-1116
[24.]
Mouthon, Tournelin P, Andre MH, et al. Polyarteritis nodosa and Churg-Strauss angiitis.
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