A propósito de um caso de imunodeficiência comum variável – Revisão das hipogamaglobulinemias | Pulmonology

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May - June 2006 A propósito de um caso de imunodeficiência comum variável – Revisão das...

Pulmonology

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Pulmonology (previously Revista Portuguesa de Pneumologia) is the official journal of the Portuguese Society of Pulmonology (Sociedade Portuguesa de Pneumologia/SPP). The journal publishes 6 issues per year, mainly about respiratory system diseases in adults and clinical research. This work can range from peer-reviewed original articles to review articles, editorials, and opinion articles. The journal is printed in English, and is freely available in its web page as well as in Medline and other databases.

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Vol. 12. Issue 3.

Pages 293-301 (May - June 2006)

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Vol. 12. Issue 3.

Pages 293-301 (May - June 2006)

DOI: 10.1016/S2173-5115(06)70404-3

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A propósito de um caso de imunodeficiência comum variável – Revisão das hipogamaglobulinemias

About a case of common variable immunodeficiency – Revision of hypogammaglobulinemias

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Alexandra Lopes*,

, Fernando Barata**, Ricardo Conceição***, Rui Pato****

* Internato Complementar de Medicina Interna, Serviço de Medicina do Centro Hospitalar de Coimbra

** Assistente Hospitalar Graduado de Pneumologia, Serviço de Pneumologia do Centro Hospitalar de Coimbra

*** Serviço de Medicina do Centro Hospitalar de Coimbra, Serviço de Pneumologia do Centro Hospitalar de Coimbra

**** Serviço de Pneumologia do Centro Hospitalar de Coimbra, Serviço de Pneumologia do Centro Hospitalar de Coimbra

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Abstract

Bibliography

Resumo

A imunodeficiência comum variável é uma imunodeficiência primária caracterizada por distúrbios imunológicos heterogéneos, de etiologia desconhecida. As suas manifestações clínicas incluem infecções recorrentes, doenças auto-imunes, hiperplasia linfóide, doenças granulomatosas e neoplasias; pode aparecer em doentes com deficiência de IgA. Os autores apresentam o caso clínico de doente com imunodeficiência comum variável e história de infecções respiratórias de repetição desde os 9 meses, associadas ao aparecimento de bronquiectasias.

Palavras-chave:

Imunodeficiência comum variável

Abstract

Common variable immunodeficiency is a primary immune deficiency characterized by heterogeneous immunologic disorders of unknown etiology. Its clinical manifestations include recurrent infections, autoimmune diseases, lymphoid hyperplasia, granulomatous diseases and malignancy. It can appear in patients with immunoglobulin A deficiency. The authors report the clinical case of a patient with common variable immunodeficiency and history of respiratory infections from the age of 9 months old, associated with the appearing of bronchiectasis.

Key-words:

Common variable immunodeficiency

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Bibliografia

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Copyright © 2006. Sociedade Portuguesa de Pneumologia

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