Journal Information
Vol. 14. Issue 4.
Pages 541-544 (July - August 2008)
Share
Share
Download PDF
More article options
Vol. 14. Issue 4.
Pages 541-544 (July - August 2008)
Caso Clínico/Clinical Case
Open Access
Amiloidose traqueobrônquica primária – A propósito de dois casos clínicos
Primary tracheobronchial amyloidosis – Two case reports
Visits
5412
Sandra Saleiro1,
Corresponding author
sandrasaleiro@portugalmail.pt

Endereço: Hospital de São João, Alameda Prof. Hernâni Monteiro, 4202-451 – Porto – Portugal Contacto.
, Venceslau Pinto Hespanhol2, Adriana Magalhães3
1 Interna Complementar de Pneumologia
2 Chefe de Serviço de Pneumologia; Director do Serviço de Pneumologia do Hospital de São João; Professor Agregado da Faculdade de Medicina da Universidade do Porto
3 Assistente Hospitalar Graduada de Pneumologia
This item has received

Under a Creative Commons license
Article information
Resumo

A amiloidose traqueobrônquica primária é uma forma de amiloidose respiratória, caracterizada pela presença de depósitos insolúveis de proteína fibrilar amilóide, ao longo da parede das vias aéreas. É uma doença pouco frequente, sendo necessário uma amostra de tecido para estabelecer o diagnóstico definitivo, com base em características histológicas específicas.

Os autores relatam dois casos clínicos de amiloidose traqueobrônquica, descrevendo os seus sintomas e os procedimentos diagnósticos e terapêuticos que foram efectuados.

Rev Port Pneumol 2008; XIV (4): 541-544

Palavras-chave:
Amiloidose
traqueobrônquica
Abstract

Primary tracheobronchial amyloidosis is a form of respiratory amyloidosis, characterised by insoluble amyloid fibril proteins deposits along the airways wall. It is an uncommon disease, requiring a tissue sample to establish the definite diagnosis based on specific pathological features.

The authors report two cases of tracheobronchial amyloidosis, describing their symptoms and the diagnostic and therapeutic procedures that were performed.

Rev Port Pneumol 2008; XIV (4): 541-544

Key-words:
Amyloidosis
tracheobronchial
Full text is only aviable in PDF
Bibliography
[1.]
M.B. Pepys, D.J. Weatherall, J.G.G. Ledingham, D.A. Warrell.
Amyloidosis.
Oxford textbook of Medicine, 3rd ed, pp. 1512-1524
[2.]
G. Husby.
Nomenclature and classification of amyloid and amyloidosis.
J Intern Med, 232 (1992), pp. 511-512
[3.]
J.D. Gillmore, P.N. Hawkins.
Amyloidosis and the respiratory tract.
Thorax, 54 (1999), pp. 444-451
[4.]
H.Y. Kim, J.G. Im, K.S. Song, et al.
Localized amyloidosis of the respiratory system: CT features.
J Comput Assist Tomogr, 23 (1999), pp. 627-631
[5.]
A. O´Regan, H.M. Fenlon, J.F. Beamis Jr., et al.
Tracheobronchial amyloidosis. The Boston University experience from 1984 to 1999.
Medicine, 79 (2000), pp. 69-79
[6.]
A.F. Flemming, A.J. Fairfax, A.G. Arnold, et al.
Treatment of endobronchial amyloidosis by intermittent bronchoscopic resection.
Br J Dis Chest, 74 (1980), pp. 183-188
[7.]
S.A. Capizzi, E. Betancourt, U.B. Prakash.
Tracheobronchial amyloidosis.
Mayo Clin Proc, 75 (2000), pp. 1148-1152
[8.]
C. Cazalets, C. Belleguic, G. Sost, et al.
Tracheobronchial amyloidosis: apropos of 2 cases.
Rev Med Interne, 23 (2002), pp. 317-321
[9.]
H. Gibbaoui, S. Abouchacra, M. Yaman.
A case of primary diffuse tracheobronchial amyloidosis.
Ann Thorac Surg, 77 (2004), pp. 1832-1834
Copyright © 2008. Sociedade Portuguesa de Pneumologia/SPP
Download PDF
Pulmonology
Article options
Tools

Are you a health professional able to prescribe or dispense drugs?