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Vol. 14. Issue 4.
Pages 541-544 (July - August 2008)
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Vol. 14. Issue 4.
Pages 541-544 (July - August 2008)
Caso Clínico/Clinical Case
Open Access
Amiloidose traqueobrônquica primária – A propósito de dois casos clínicos
Primary tracheobronchial amyloidosis – Two case reports
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Sandra Saleiro1,
Corresponding author
sandrasaleiro@portugalmail.pt

Endereço: Hospital de São João, Alameda Prof. Hernâni Monteiro, 4202-451 – Porto – Portugal Contacto.
, Venceslau Pinto Hespanhol2, Adriana Magalhães3
1 Interna Complementar de Pneumologia
2 Chefe de Serviço de Pneumologia; Director do Serviço de Pneumologia do Hospital de São João; Professor Agregado da Faculdade de Medicina da Universidade do Porto
3 Assistente Hospitalar Graduada de Pneumologia
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Resumo

A amiloidose traqueobrônquica primária é uma forma de amiloidose respiratória, caracterizada pela presença de depósitos insolúveis de proteína fibrilar amilóide, ao longo da parede das vias aéreas. É uma doença pouco frequente, sendo necessário uma amostra de tecido para estabelecer o diagnóstico definitivo, com base em características histológicas específicas.

Os autores relatam dois casos clínicos de amiloidose traqueobrônquica, descrevendo os seus sintomas e os procedimentos diagnósticos e terapêuticos que foram efectuados.

Rev Port Pneumol 2008; XIV (4): 541-544

Palavras-chave:
Amiloidose
traqueobrônquica
Abstract

Primary tracheobronchial amyloidosis is a form of respiratory amyloidosis, characterised by insoluble amyloid fibril proteins deposits along the airways wall. It is an uncommon disease, requiring a tissue sample to establish the definite diagnosis based on specific pathological features.

The authors report two cases of tracheobronchial amyloidosis, describing their symptoms and the diagnostic and therapeutic procedures that were performed.

Rev Port Pneumol 2008; XIV (4): 541-544

Key-words:
Amyloidosis
tracheobronchial
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Copyright © 2008. Sociedade Portuguesa de Pneumologia/SPP
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