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Vol. 15. Issue 2.
Pages 331-337 (March - April 2009)
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Vol. 15. Issue 2.
Pages 331-337 (March - April 2009)
Caso Clínico/Case Report
Open Access
Telangiectasia hemorrágica hereditária e malformações arteriovenosas pulmonares – Embolização com rolhão vascular Amplatzer
Hereditary hemorrhagic telangiectasia and pulmonary arteriovenous malformations – Embolization with Amplatzer vascular plug
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Cláudia Sofia Santos1, Ana Norte1, Ilda Ferreira2, Paulo Almeida3, A. Segorbe Luís4, Mário Loureiro5, M. Fontes Baganha6
1 Interna Complementar de Pneumologia
2 Assistente Hospitalar Graduada de Pneumologia
3 Assistente Hospitalar Graduado de Imagiologia
4 Chefe de Serviço de Pneumologia dos HUC
5 Director do Serviço de Pneumologia dos HUC
6 Director do Departamento de Ciências Pneumológicas e Alergológicas dos HUC
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Resumo

As malformações arteriovenosas pulmonares (MAVP) estão associadas a telangiectasia hemorrágica hereditária em cerca de 70% dos casos, podendo cursar com complicações neurológicas graves decorrentes do em-bolismo paradoxal potencial. A terapêutica das malformações é realizada no sentido de prevenir estas complicações.

Descreve-se o caso clínico de uma doente com duas MAVP, no contexto de telangiectasia hemorrágica hereditária, submetida a embolização com o rolhão vascular Amplatzer. Este novo dispositivo é cada vez mais utilizado nestas situações, salientando-se algumas das suas características e vantagens em relação a outras técnicas de embolização mais frequentemente utiliza-das.

Rev Port Pneumol 2009; XV (2): 331-337

Palavras-chave:
Malformação arteriovenosa pulmonar
telangiectasia hemorrágica hereditária
rolhão vascular Amplatzer
Abstract

Pulmonary arteriovenous malformations (PAVMs) are associated to hereditary hemorrhagic telangiectasia in about 70% of the cases. PAVMs are associated to serious neurologic complications, secondary to inherent paradoxical embolisms. Treatment of the malformations is done to prevent these complications.

The authors report a clinical case of a patient with two PAVMs, with hereditary hemorrhagic telangiectasia, who was treated by embolization with an Amplatzer vascular plug, a new device increasingly used in these situations. The authors emphasise some of its characteristics and advantages when compared with other embolization techniques most commonly used.

Rev Port Pneumol 2009; XV (2): 331-337

Key-words:
Pulmonary arteriovenous malformations
hereditary hemorrhagic telangiectasia
Amplatzer vascular plug
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Copyright © 2009. Sociedade Portuguesa de Pneumologia/SPP
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